TY  - JOUR
AU  - Oller, Jorge
AU  - Gabandé-Rodriguez, Enrique
AU  - Ruiz-Rodríguez, Maria Jesús
AU  - Desdín-Micó, Gabriela
AU  - Aranda Gómez, Juan Francisco
AU  - Ballesteros-Rodríguez, Constanza
AU  - Blanco, Eva Maria
AU  - Roldán-Montero, Raquel
AU  - Acuña, Pedro
AU  - Forteza-Gil, Alberto
AU  - Martín-López, Carlos
AU  - Nistal, Francisco
AU  - Lino Cardenas, Christian
AU  - Evan, Lindsay
AU  - Martín-Vertura, Jose Luis
AU  - Briones, Ana 
AU  - Redondo, Juan Miguel
AU  - Mittelbrunn, María
PY  - 2021
DO  - 10.1161/CIRCULATIONAHA.120.051171
SN  - 0009-7322
UR  - https://hdl.handle.net/20.500.14352/94925
T2  - Circulation
AB  - Background: Marfan syndrome (MFS) is an autosomal dominant disorder of the connective tissue caused by mutations in the FBN1 (fibrillin-1) gene encoding a large glycoprotein in the extracellular matrix called fibrillin-1. The major complication of...
LA  - eng
M2  - 2091
KW  - Aortic aneurysm
KW  - DNA
KW  - Mitochondrial
KW  - Extracellular matrix
KW  - Genetic diseases
KW  - Inborn
KW  - Glycolysis
KW  - Marfan syndrome
KW  - Muscle
KW  - Smooth
KW  - Vascular
TI  - Extracellular Tuning of Mitochondrial Respiration Leads to Aortic Aneurysm
TY  - journal article
VL  - 143
ER  -