TY - JOUR AU - Herranz Martín, Saúl AU - Azzouz, Mimoun PY - 2017 DO - 10.1242/dmm.029892 SN - 1754-8411 SN - 1754-8403 UR - https://hdl.handle.net/20.500.14352/95721 T2 - Disease Models & Mechanisms AB - Intronic GGGGCC repeat expansions in C9orf72 are the most common genetic cause of amyotrophic lateral sclerosis (ALS) and frontotemporal dementia (FTD). Two major pathologies stemming from the hexanucleotide RNA expansions (HREs) have been identified... LA - eng M2 - 859 PB - The Company of Biologists KW - C9orf72 KW - Neurodegeneration KW - ALS/FTD KW - Mouse model KW - C9RAN aggregates TI - Viral delivery of C9ORF72 hexanucleotide repeat expansions in mice lead to repeat length dependent neuropathology and behavioral deficits TY - journal article VL - 10 ER -