TY  - JOUR
AU  - Aguado Sánchez, Tania
AU  - García, Marta
AU  - García, Adela
AU  - Ferrer-Mayorga, Gemma
AU  - Martínez-Santamaría, Lucía
AU  - Río, Marcela del
AU  - Botella, Luisa-María
AU  - Sánchez-Puelles, José-María
PY  - 2020
DO  - 10.3390/cells9092108
SN  - 2073-4409
UR  - https://hdl.handle.net/20.500.14352/91527
AB  - Recessive dystrophic epidermolysis bullosa (RDEB) is a severe skin disease caused by mutation of the COL7A1 gene. RDEB is associated with high levels of TGF-β1, which is likely to be involved in the fibrosis that develops in this disease. Endoglin...
LA  - eng
M2  - 1
PB  - MDPI
KW  - Epidermolysis bullosa
KW  - TGF-fibrosis
KW  - Raloxifene
KW  - N-acetylcysteine
KW  - Endoglin
KW  - Smad
KW  - ALK1/5
KW  - Drug repurposing
TI  - Raloxifene and n-Acetylcysteine Ameliorate TGF-Signalling in Fibroblasts from Patients with Recessive Dominant Epidermolysis Bullosa
TY  - journal article
VL  - 9
ER  -