TY - JOUR AU - López-Nevado, Marta AU - González Granado, Luis Ignacio AU - Ruiz Contreras, Jesús AU - Paz Artal, Estela Natividad AU - Allende Martínez, Luis Miguel PY - 2021 DO - 10.3389/fimmu.2021.671755 SN - 1664-3224 UR - https://hdl.handle.net/20.500.14352/114143 T2 - Frontiers Immunology AB - Primary immune regulatory disorders (PIRD) are associated with autoimmunity, autoinflammation and/or dysregulation of lymphocyte homeostasis. Autoimmune lymphoproliferative syndrome (ALPS) is a PIRD due to an apoptotic defect in Fas-FasL pathway and... LA - eng KW - Inmunología KW - regulación inmunitaria primaria KW - evaluación inmunológica TI - Primary Immune Regulatory Disorders With an Autoimmune Lymphoproliferative Syndrome-Like Phenotype: Immunologic Evaluation, Early Diagnosis and Management TY - journal article VL - 12 ER -