TY - JOUR AU - Padrón-Barthe, Laura AU - Gómez-Salinero, Jesús M. AU - Domínguez, Fernando AU - Román, Marta AU - Larrasa-Alonso, Javier AU - Martínez, Fernando AU - López-Olañeta, Marina AU - Bonzón-Kulichenko, Elena AU - Vázquez, Jesús AU - Martí-Gómez, Carlos AU - Santiago, Demetrio J. AU - Prados, Belén AU - Giovinazzo, Giovanna AU - Gómez-Gaviro, María Victoria AU - Priori, Silvia AU - Garcia-Pavia, Pablo AU - Lara-Pezzi, Enrique AU - Villalba Orero, María AU - Ortiz Sánchez, Paula PY - 2019 DO - 10.1161/circulationaha.119.040366 SN - 0009-7322 SN - 1524-4539 UR - https://hdl.handle.net/20.500.14352/95164 T2 - Circulation AB - BACKGROUND: Arrhythmogenic cardiomyopathy/arrhythmogenic right ventricular cardiomyopathy (ARVC) is an inherited cardiac disease characterized by fibrofatty replacement of the myocardium, resulting in heart failure and sudden cardiac death. The most... LA - eng M2 - 1188 PB - American Heart Association KW - arrhythmogenic right ventricular dysplasia KW - calcineurin KW - GSK3β KW - therapy KW - TMEM43 TI - Severe Cardiac Dysfunction and Death Caused by Arrhythmogenic Right Ventricular Cardiomyopathy Type 5 Are Improved by Inhibition of Glycogen Synthase Kinase-3β TY - journal article VL - 140 ER -