TY - JOUR AU - Rodríguez Sousa, Antonio Alberto AU - Barandica Fernández, Jesús María AU - Miller, Jonathan AU - Mir Montejano, Matías PY - 2018 DO - 10.1007/s11517-018-1885-1 SN - 0140-0118, ESSN: 1741-0444 UR - https://hdl.handle.net/20.500.14352/13209 T2 - Medical and Biological Engineering and Computing AB - Cystic fibrosis is an inherited disorder of the cystic fibrosis transmembrane conductance regulator gene (CFTR) that affects the respiratory system. Current treatment is palliative, but there is a gene therapy under investigation which involves... LA - eng M2 - 413 PB - Sringer Verlag KW - CFTR protein (cystic fibrosis transmembrane conductance regulator) KW - Dynamic modeling KW - Genetic therapy KW - Pulmonary function KW - Respiratory physiology TI - Physiological study of pulmonary involvement in adults with cystic fibrosis through simulated modeling of different clinical scenarios TY - journal article VL - 57 ER -