TY  - JOUR
AU  - Esmaili, Soha
AU  - Rodríguez Hermosa, Juan Luis
AU  - Vargas Centanaro, Gianna
AU  - Álvarez-Sala Walther, José Luis
AU  - Esmaili, Iman
AU  - Calle Rubio, Myrian
PY  - 2025
DO  - 10.3390/biom15040599
SN  - 2218-273X
UR  - https://hdl.handle.net/20.500.14352/130019
T2  - Biomolecules
AB  - Background: Alpha-1 antitrypsin deficiency (AATD) is a genetic disorder associated with an increased risk of developing chronic obstructive pulmonary disease (COPD) with variable phenotypic expression among different genotypes. While the PiZZ genotype...
LA  - eng
PB  - MDPI
KW  - Alpha-1 antitrypsin deficiency
KW  - PiSZ genotype
KW  - PiZZ genotype
KW  - Augmentation therapy
KW  - Lung densitometry
TI  - Progression and Augmentation Therapy in PiSZ and PiZZ Alpha-1 Antitrypsin Deficiency: a Longitudinal Functional and Densitometric Study
TY  - journal article
VL  - 15
ER  -